소아에서의 축삭형 길랑-바레 증후군 1예

A five-year old boy visited electrodiagnostic clinic presenting Gower’s sign. There were weakness of both lower extremities and absent muscle stretch reflexes in the lower extremities. On initial electrodiagnostic test, the sensory nerve conduction study revealed low amplitude in the median and ulnar nerves in spite of normal amplitude in sural nerve. Initial diagnosis was acute motor sensory axonal neuropathy. There was albuminocytologic dissociation in the cerebrospinal fluid study and enhancement at the ventral nerve roots below T8, 9 level in the spine magnetic resonance imaging. The follow-up electrodiagnostic study presented a demyelinating criteria: delayed conduction velocity and distal latency. We pointed out a need of follow-up study for the diagnosis of Guillain-Barre syndrome (GBS) subtypes. GBS subtypes can be diagnosed by motor or sensory conduction criteria even though there has been argument. We report this case with review of the literatures.